Clinical and laboratory findings

Anti-ARS

Anti-CADM-140/MDA5

Anti-Mi-2

Anti-p155/TIF1-γ

Negative

(n = 27)

(n = 19)

(n = 5)

(n = 8)

(n = 36)

Age at onset (mean ± SD)

52 ± 14

53 ± 13

55 ± 17

62 ± 20

51 ± 14

Male/female

8/19

5/14

2/3

2/6

7/29

Gottron’s sign or papules (%)

67

84

80

88

78

Heliotrope rash (%)

37

37

80

38

56

V-sign or Shawl-sign (%)

15

37

40

63

31

Muscle weakness (%)

93

11

100

88

81

Elevation of CK (%)

93

26

100

88

78

Fever (%)

63

68

20

25

53

Arthritis (%)

81

79

60

13

50

Raynaud’s phenomenon (%)

30

5

0

13

6

ILD (%)

81

89

0

13

50

Rapidly progressive ILD (%)

7

84

0

0

8

Malignancy (%)

7

5

0

75

19

ANA (FANA) (%)

44

16

100

88

36